Targeting the METTL1/m7G axis as a therapeutic strategy in myeloid leukemia

L Lili Ren H Honghai Zhang O Olga Bobileva (4Latvian Institute of Organic Synthesis, Riga, Latvia) F Francesco Nai (5Department of Biochemistry, University of Zurich, Zurich, Switzerland) H Hongjie Bi A Anthony Chan G Genevieve E. Baker (6Department of Cancer Biology and Molecular Medicine, Beckman Research Institute of City of Hope, Duarte, CA) L Lei Dong (Quantitative Biomedical Research Center, University of Texas Southwestern Medical Center, Dallas, TX, USA.) D David Guarin (8Department of Biochemistry, University of Texas Southwestern Medical Center, Dallas, TX) W Weidong Hu W Wei Li I Irena Leite (4Latvian Institute of Organic Synthesis, Riga, Latvia) X Xueer Wang X Xiaoxu Zhang (State Key Laboratory of Photoelectric Conversion and Utilization of Solar Energy, Qingdao New Energy Shandong Laboratory, Qingdao Institute of Bioenergy and Bioprocess Technology) M Meilin Xue H Haixia Wang H Hanjun Qin X Xiwei Wu L Lucy Ghoda L Lin Xu (Harold C. Simmons Comprehensive Cancer Center, University of Texas Southwestern Medical Center, Dallas, TX, USA.) B Bin Zhang L Ling Li M Mark Wunderlich J James C. Mulloy C Courtney L. Jones (12Division of Experimental Hematology and Cancer Biology, Cincinnati Children's Hospital Medical Center, Cincinnati, OH) S Seán E. O’Leary (13Department of Biochemistry, University of California Riverside, Riverside, CA) H Hongzhi Li S Steven T. Rosen C Chun-Wei David Chen (1Department of Systems Biology, Beckman Research Institute of City of Hope, Monrovia, CA) N Nora Heisterkamp J J. Jefferson P. Perry (6Department of Cancer Biology and Molecular Medicine, Beckman Research Institute of City of Hope, Duarte, CA) Y Yunsun Nam J Jianjun Chen (State Key Joint Laboratory of Environment Simulation and Pollution Control, School of Environment) A Amedeo Caflisch X Xiaobo Li R Rui Su

Abstract

Abstract N7-methylguanosine (m7G), a prevalent modification in transfer RNAs (tRNAs), is primarily catalyzed by the methyltransferase METTL1. Although growing evidence supports a role for METTL1 in various tumors, its therapeutic potential and precise function in leukemia stem cell (LSC) homeostasis remain largely unexplored. Here, we identify METTL1 as a key regulator of LSC self-renewal and homing within bone marrow (BM) microenvironment through catalyzing m7G formation on a specific tRNA, tRNAPheGAA, thereby promoting leukemogenesis. Mechanistically, METTL1 loss significantly reduces m7G abundance and steady-state levels of tRNAPheGAA, leading to translation suppression and degradation of transcripts enriched with tRNAPheGAA-related codons, such as hematopoietic cell kinase (HCK). Decreased HCK expression disrupts CXCR4 signaling, impairing LSC self-renewal and BM homing. Therapeutically, we characterized a small-molecule METTL1 inhibitor (M1i; NSC137443), through high-throughput screening. Pharmacological inhibition of METTL1 demonstrated potent antitumor efficacy by reducing tRNA m7G levels and disrupting the tRNAPheGAA/HCK/CXCR4 cascade. Notably, targeting METTL1 significantly reduces LSC frequency, delays leukemogenesis, and prolongs survival in multiple acute myeloid leukemia models. Together, our findings establish a previously unrecognized role for METTL1 and its target tRNAPheGAA in LSC homeostasis and provide compelling proof-of-concept evidence that METTL1 is a druggable epitranscriptomic target for antileukemia therapy.

Article Details

Journal Blood
Volume / Issue Vol. 147, Issue 25
Published June 18, 2026
Pages 3069-3085
ISSN 0006-4971
Publisher Elsevier BV

Journal Info

Blood

Elsevier BV

ISSN: 0006-4971 Health Sciences

Authors (36)

L

Lili Ren

H

Honghai Zhang

O

Olga Bobileva

4Latvian Institute of Organic Synthesis, Riga, Latvia

F

Francesco Nai

5Department of Biochemistry, University of Zurich, Zurich, Switzerland

H

Hongjie Bi

A

Anthony Chan

G

Genevieve E. Baker

6Department of Cancer Biology and Molecular Medicine, Beckman Research Institute of City of Hope, Duarte, CA

L

Lei Dong

Quantitative Biomedical Research Center, University of Texas Southwestern Medical Center, Dallas, TX, USA.

D

David Guarin

8Department of Biochemistry, University of Texas Southwestern Medical Center, Dallas, TX

W

Weidong Hu

W

Wei Li

I

Irena Leite

4Latvian Institute of Organic Synthesis, Riga, Latvia

X

Xueer Wang

X

Xiaoxu Zhang

State Key Laboratory of Photoelectric Conversion and Utilization of Solar Energy, Qingdao New Energy Shandong Laboratory, Qingdao Institute of Bioenergy and Bioprocess Technology

M

Meilin Xue

H

Haixia Wang

H

Hanjun Qin

X

Xiwei Wu

L

Lucy Ghoda

L

Lin Xu

Harold C. Simmons Comprehensive Cancer Center, University of Texas Southwestern Medical Center, Dallas, TX, USA.

B

Bin Zhang

L

Ling Li

M

Mark Wunderlich

J

James C. Mulloy

C

Courtney L. Jones

12Division of Experimental Hematology and Cancer Biology, Cincinnati Children's Hospital Medical Center, Cincinnati, OH

S

Seán E. O’Leary

13Department of Biochemistry, University of California Riverside, Riverside, CA

H

Hongzhi Li

S

Steven T. Rosen

C

Chun-Wei David Chen

1Department of Systems Biology, Beckman Research Institute of City of Hope, Monrovia, CA

N

Nora Heisterkamp

J

J. Jefferson P. Perry

6Department of Cancer Biology and Molecular Medicine, Beckman Research Institute of City of Hope, Duarte, CA

Y

Yunsun Nam

J

Jianjun Chen

State Key Joint Laboratory of Environment Simulation and Pollution Control, School of Environment

A

Amedeo Caflisch

X

Xiaobo Li

R

Rui Su