Proteasomal processing of the viral replicase ORF1 facilitates HEV-induced liver fibrosis

F Fei Zhang L Ling-Dong Xu (Department of Hepatobiliary and Pancreatic Surgery and Zhejiang Provincial Key Laboratory of Pancreatic Disease, The First Affiliated Hospital, Zhejiang University School of Medicine) S Shiying Wu (Ministry of Education Laboratory of Biosystems Homeostasis & Protection, Zhejiang Provincial Key Laboratory for Cancer Molecular Cell Biology, Life Sciences Institute, Zhejiang University) Q Qirou Wu (Department of Hepatobiliary and Pancreatic Surgery and Zhejiang Provincial Key Laboratory of Pancreatic Disease, The First Affiliated Hospital, Zhejiang University School of Medicine) A Ailian Wang (Department of Hepatobiliary and Pancreatic Surgery and Zhejiang Provincial Key Laboratory of Pancreatic Disease, The First Affiliated Hospital, Zhejiang University School of Medicine) S Shengduo Liu (Institute of Intelligent Medicine, ZJU-Hangzhou Global Scientific and Technological Innovation Center, Zhejiang University) Q Qian Zhang X Xinyuan Yu (Ministry of Education Laboratory of Biosystems Homeostasis & Protection, Zhejiang Provincial Key Laboratory for Cancer Molecular Cell Biology, Life Sciences Institute, Zhejiang University) B Bin Wang Y Yinghao Pan (Ministry of Education Laboratory of Biosystems Homeostasis & Protection, Zhejiang Provincial Key Laboratory for Cancer Molecular Cell Biology, Life Sciences Institute, Zhejiang University) F Fei Huang D Dante Neculai (Department of Cell Biology Zhejiang University School of Medicine) B Bing Xia X Xin-Hua Feng (Ministry of Education Laboratory of Biosystems Homeostasis & Protection, Zhejiang Provincial Key Laboratory for Cancer Molecular Cell Biology, Life Sciences Institute, Zhejiang University) L Li Shen Q Qi Zhang T Tingbo Liang Y Yao-Wei Huang (State Key Laboratory for Animal Disease Control and Prevention, South China Agricultural University) P Pinglong Xu (Department of Hepatobiliary and Pancreatic Surgery and Zhejiang Provincial Key Laboratory of Pancreatic Disease, The First Affiliated Hospital, Zhejiang University School of Medicine)

Abstract

Chronic infections with hepatitis E virus (HEV), especially those of genotype 3 (G3), frequently lead to liver fibrosis and cirrhosis in patients. However, the causation and mechanism of liver fibrosis triggered by chronic HEV infection remain poorly understood. Here, we found that the viral multiple-domain replicase (ORF1) undergoes unique ubiquitin–proteasomal processing leading to formation of the H EV- D erived S MAD A ctivator (HDSA), a viral polypeptide lacking putative helicase and RNA polymerase domains. The HDSA is stable, non-HSP90-bound, localizes to the nucleus, and is abundant in G3 HEV-infected hepatocytes of various origins. Markedly, the HDSA in hepatocytes potentiates the fibrogenic TGF-β/SMAD pathway by forming compact complexes with SMAD3 to facilitate its promoter binding and coactivator recruitment, leading to significant fibrosis in HEV-susceptible gerbils. Virus infection–induced liver fibrosis in HEV-susceptible gerbils could be prevented by mutating the residues P989C, A990C, and A991C (PAA-3C) within ORF1, which are required for proteasomal processing. Thus, we have identified a viral protein derived from host proteasomal processing, defined its notable role in liver fibrosis and highlighted the nature of an unanticipated host–HEV interaction that facilitates hepatitis E pathogenesis.

Article Details

Volume / Issue Vol. 122, Issue 11
Published March 18, 2025
ISSN 0027-8424
Publisher National Academy of Sciences

Authors (19)

F

Fei Zhang

L

Ling-Dong Xu

Department of Hepatobiliary and Pancreatic Surgery and Zhejiang Provincial Key Laboratory of Pancreatic Disease, The First Affiliated Hospital, Zhejiang University School of Medicine

S

Shiying Wu

Ministry of Education Laboratory of Biosystems Homeostasis & Protection, Zhejiang Provincial Key Laboratory for Cancer Molecular Cell Biology, Life Sciences Institute, Zhejiang University

Q

Qirou Wu

Department of Hepatobiliary and Pancreatic Surgery and Zhejiang Provincial Key Laboratory of Pancreatic Disease, The First Affiliated Hospital, Zhejiang University School of Medicine

A

Ailian Wang

Department of Hepatobiliary and Pancreatic Surgery and Zhejiang Provincial Key Laboratory of Pancreatic Disease, The First Affiliated Hospital, Zhejiang University School of Medicine

S

Shengduo Liu

Institute of Intelligent Medicine, ZJU-Hangzhou Global Scientific and Technological Innovation Center, Zhejiang University

Q

Qian Zhang

X

Xinyuan Yu

Ministry of Education Laboratory of Biosystems Homeostasis & Protection, Zhejiang Provincial Key Laboratory for Cancer Molecular Cell Biology, Life Sciences Institute, Zhejiang University

B

Bin Wang

Y

Yinghao Pan

Ministry of Education Laboratory of Biosystems Homeostasis & Protection, Zhejiang Provincial Key Laboratory for Cancer Molecular Cell Biology, Life Sciences Institute, Zhejiang University

F

Fei Huang

D

Dante Neculai

Department of Cell Biology Zhejiang University School of Medicine

B

Bing Xia

X

Xin-Hua Feng

Ministry of Education Laboratory of Biosystems Homeostasis & Protection, Zhejiang Provincial Key Laboratory for Cancer Molecular Cell Biology, Life Sciences Institute, Zhejiang University

L

Li Shen

Q

Qi Zhang

T

Tingbo Liang

Y

Yao-Wei Huang

State Key Laboratory for Animal Disease Control and Prevention, South China Agricultural University

P

Pinglong Xu

Department of Hepatobiliary and Pancreatic Surgery and Zhejiang Provincial Key Laboratory of Pancreatic Disease, The First Affiliated Hospital, Zhejiang University School of Medicine