PPT1 is a negative regulator of STING signaling in cancer cells and its inhibition reactivates immune surveillance in cold tumors

S Shreya R. Chowdhury (Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School) C Chaitanya N. Parikh (Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School) A Arshia N. Kaur (Department of Systems Biology, University of Massachusetts) K Kelly D. DeMarco (Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School) H Hadiya K. Giwa (Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School) A Alok K. Mishra (Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School) K Katherine C. Murphy (Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School) L Lin Zhou B Boyang Ma (Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School) T Tianyi Ye (Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School) J Junhui Li (Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School) H Haibo Liu (Discovery & Development Sciences) S Shi Bai (Department of Pathology, University of Massachusetts Medical Center) C Calvin Johnson (Division of Hematology-Oncology, University of Massachusetts Chan Medical School) K Karl Simin (Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School) J Jason R. Pitarresi (Division of Hematology-Oncology, University of Massachusetts Chan Medical School) L Lihua Julie Zhu (Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School) E Emma V. Watson (Department of Systems Biology, University of Massachusetts) M Michelle A. Kelliher (Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School) M Michael R. Green K Katherine A. Fitzgerald (Department of Medicine, University of Massachusetts Chan Medical School) M Marcus Ruscetti (Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School)

Abstract

Immunotherapy modalities have revolutionized cancer treatment for a number of metastatic and treatment-refractory tumor types. Still, many malignancies that lack T cell infiltration and are termed immunologically “cold” fail to respond to these modalities. One approach to increase tumor immunogenicity has been to induce stimulator of interferon gene (STING) and downstream interferon signaling that is often dysregulated in cold tumors. Despite some early success of STING agonists in preclinical cancer models, these approaches have not been successful in the clinic due to poor tumor penetrance and systemic toxicities. Here, we performed a genome-wide CRISPR screen to uncover therapeutic targets to activate STING expression in human tumors. We identified the lysosomal hydrolase Palmitoyl Protein Thioesterase1 (PPT1) as a negative regulator of STING highly expressed in cold ovarian and prostate tumors. Genetic or pharmacological PPT1 suppression increased STING protein stability and its downstream activation of interferon and inflammatory cytokine signaling to enhance T cell migration. Treatment of preclinical prostate and ovarian cancer models expressing low levels of STING with the small molecule PPT1 inhibitor GNS561 enhanced STING expression and activation, leading to infiltration and activation of cytotoxic T cells that turned these tumors “hot” and reduced tumor growth, fibrosis, and dissemination without toxicity. Further analysis demonstrated that PPT1 is associated with reduced STING expression, CD8 + T cell numbers, overall survival, and immunotherapy outcomes in ovarian and prostate cancer patients. Thus, PPT1 inhibition may be a promising approach to activate STING and potentiate the effects of immunotherapy in cold tumors.

Article Details

Volume / Issue Vol. 122, Issue 39
Published September 30, 2025
ISSN 0027-8424
Publisher National Academy of Sciences

Authors (22)

S

Shreya R. Chowdhury

Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School

C

Chaitanya N. Parikh

Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School

A

Arshia N. Kaur

Department of Systems Biology, University of Massachusetts

K

Kelly D. DeMarco

Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School

H

Hadiya K. Giwa

Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School

A

Alok K. Mishra

Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School

K

Katherine C. Murphy

Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School

L

Lin Zhou

B

Boyang Ma

Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School

T

Tianyi Ye

Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School

J

Junhui Li

Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School

H

Haibo Liu

Discovery & Development Sciences

S

Shi Bai

Department of Pathology, University of Massachusetts Medical Center

C

Calvin Johnson

Division of Hematology-Oncology, University of Massachusetts Chan Medical School

K

Karl Simin

Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School

J

Jason R. Pitarresi

Division of Hematology-Oncology, University of Massachusetts Chan Medical School

L

Lihua Julie Zhu

Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School

E

Emma V. Watson

Department of Systems Biology, University of Massachusetts

M

Michelle A. Kelliher

Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School

M

Michael R. Green

K

Katherine A. Fitzgerald

Department of Medicine, University of Massachusetts Chan Medical School

M

Marcus Ruscetti

Department of Molecular, Cell, and Cancer Biology, University of Massachusetts Chan Medical School