Nivolumab ± Ipilimumab in Patients With Pretreated Advanced Neuroendocrine Carcinoma: The GCO-001 NIPINEC Randomized Phase II Trial

T Thomas Pierre Walter (Medical Oncology Department, Edouard Herriot Hospital, Lyon, France) J Julien Mazières (Centre Hospitalier Universitaire de Toulouse, Université Paul Sabatier, Toulouse, France) J Josiane Otto (Department of Medical Oncology, Centre Antoine-Lacassagne, Nice, France) H Hervé Lena (Pneumology Department, Centre Hospitalier Universitaire Rennes, Université Rennes 1, INSERM, UMR_S 1242, Centre Eugene Marquis, Rennes, France) C Côme Lepage (Gastroenterology & Digestive Oncology, Dijon University Hospital Le Bocage, Dijon, France) D Denis Smith (Hepatogastroenterology & Digestive Oncology Bordeaux University Hospital, Bordeaux, France) J Jeannick Madelaine (Department of Pneumology, Caen University Hospital, Caen, France) L Laurence Gérinière (Respiratory Diseases and Thoracic Oncology Department, Lyon Sud Hospital, Cancer Institute of Hospices Civils de Lyon, Lyon, France) T Thomas Egenod (Pneumology Department, Limoges University Hospital, Limoges, France) F Farid El Hajbi (Oncology Department, Oscar Lambret Centre, Lille, France) A Aurélie Ferru (Department of Abdominal Oncology, University Hospital of Poitiers, Poitiers, France) C Christelle Clément-Duchene (Department of Pneumology, Lorraine Cancer Institute, Vandoeuvre-les-Nancy, France) A Anne Madroszyk (Medical Oncology Department, Paoli-Calmettes Institute, Marseille, France) T Thibault Brotelle (Medical Oncology Department, Avignon Hospital, Avignon, France) K Karine Bouhier-Leporrier J Jérôme Desrame (Oncology Department, Jean Mermoz Private Hospital, Lyon, France) F François Ghiringhelli N Nicolas Paleiron (Pneumology Department, Saint-Anne Military Teaching Hospital, Toulon, France) A Antoine Khalil (Department of Radiology, Neuroradiology Unit, Assistance Publique-Hôpitaux de Paris, Bichat-Claude Bernard University Hospital, Paris, France) L Laurent Milot (Body and VIR Radiology Department, Hospices Civils de Lyon, Hospital Edouard Herriot, Lyon, France) O Olivier Chevallier (Department of Radiology, Section of Musculoskeletal Imaging and Intervention, LE2I UMR CNRS 6306, François-Mitterrand University Hospital, Dijon, France) A Anne Couvelard (Department of Pathology, Assistance Publique-Hôpitaux de Paris, Bichat-Claude Bernard University Hospital, Paris, France) S Sylvie Lantuejoul (Department of Biopathology, Léon Bérard Centre, Lyon, France) A Alexandra Langlais (Clinical Research Unit, Intergroupe Francophone de Cancérologie Thoracique, Paris, France) F Franck Morin M Michaël Duruisseaux (Respiratory Department and Early Phase (EPSILYON), Louis Pradel Hospital, Hospices Civils de Lyon Cancer Institute, Lyon, France) P Pierre Michel (Hepatogastroenterology Department, Rouen University Hospital, Rouen, France) C Christophe Louvet (Department of Medical Oncology, Institut Mutualiste Montsouris, Paris, France) V Virginie Westeel (Pneumology department, CHU Besançon - Hôpital J. MINJOZ, Besançon, France) N Nicolas Girard (Institut Curie, Institut du Thorax Curie-Montsouris, Paris)

Abstract

PURPOSE There is no standard second-line therapy for gastroenteropancreatic (GEP) and lung large-cell neuroendocrine carcinoma (NEC) after the failure of platinum-based chemotherapy. This study aimed to investigate the efficacy of nivolumab ± ipilimumab. METHODS The GCO-001-NIPINEC (ClinicalTrials.gov identifier: NCT03591731 ) trial was a noncomparative, open-label, phase II trial. The main inclusion criteria were age ≥18 years, performance status (PS) ≤2, advanced large- and small-cell GEP-NEC and large-cell lung NEC, and second- or third-line treatment for NECs refractory to platinum-based chemotherapy. Patients were randomly assigned (1:1) and stratified by age and PS to receive nivolumab (3 mg/kg/once every 2 weeks) ± ipilimumab (1 mg/kg/once every 6 weeks) for 2 years or until progression or unacceptable toxicity. The primary end point was objective response rate (ORR) at 8 weeks, assessed by investigators. RESULTS A total of 185 patients (91 in the nivolumab arm and 94 in the nivolumab-ipilimumab arm) were enrolled between December 2018 and March 2021; 169 were analyzed (median age of 64.5 years, 71% male, 91% PS 0-1). The main primary tumor locations were lungs (50%), colorectal (15%), gastroesophageal (14%), and pancreatic (13%) regions. The ORR at 8 weeks was 7.2% (95% CI, 2.7 to 15.1]) in the nivolumab arm and 14.0% (95% CI, 7.4 to 23.1) in the nivolumab-ipilimumab arm. The best ORR was 9.6% and 20.9%, respectively, whereas the median progression-free and overall survival were approximately 2 months and 6 months in both arms. One treatment-related death occurred, in the nivolumab arm. The grade 3-4 adverse events (≥5%) were asthenia (13%), gamma-glutamyl transferase increase (10%), alkaline phosphatase increase (9%), dyspnea (7%), and anemia (6%) in the nivolumab-ipilimumab arm. CONCLUSION Nivolumab-ipilimumab could be a second-/third-line treatment option for patients with NECs. However, given the limited magnitude of benefit, studies are warranted to evaluate its use earlier and/or associated with chemotherapy.

Article Details

Volume / Issue Vol. 44, Issue 12
Published April 20, 2026
Pages 1120-1129
ISSN 0732-183X
Publisher Lippincott Williams & Wilkins

Journal Info

Journal of Clinical Oncology

Lippincott Williams & Wilkins

ISSN: 0732-183X Health Sciences

Authors (30)

T

Thomas Pierre Walter

Medical Oncology Department, Edouard Herriot Hospital, Lyon, France

J

Julien Mazières

Centre Hospitalier Universitaire de Toulouse, Université Paul Sabatier, Toulouse, France

J

Josiane Otto

Department of Medical Oncology, Centre Antoine-Lacassagne, Nice, France

H

Hervé Lena

Pneumology Department, Centre Hospitalier Universitaire Rennes, Université Rennes 1, INSERM, UMR_S 1242, Centre Eugene Marquis, Rennes, France

C

Côme Lepage

Gastroenterology & Digestive Oncology, Dijon University Hospital Le Bocage, Dijon, France

D

Denis Smith

Hepatogastroenterology & Digestive Oncology Bordeaux University Hospital, Bordeaux, France

J

Jeannick Madelaine

Department of Pneumology, Caen University Hospital, Caen, France

L

Laurence Gérinière

Respiratory Diseases and Thoracic Oncology Department, Lyon Sud Hospital, Cancer Institute of Hospices Civils de Lyon, Lyon, France

T

Thomas Egenod

Pneumology Department, Limoges University Hospital, Limoges, France

F

Farid El Hajbi

Oncology Department, Oscar Lambret Centre, Lille, France

A

Aurélie Ferru

Department of Abdominal Oncology, University Hospital of Poitiers, Poitiers, France

C

Christelle Clément-Duchene

Department of Pneumology, Lorraine Cancer Institute, Vandoeuvre-les-Nancy, France

A

Anne Madroszyk

Medical Oncology Department, Paoli-Calmettes Institute, Marseille, France

T

Thibault Brotelle

Medical Oncology Department, Avignon Hospital, Avignon, France

K

Karine Bouhier-Leporrier

J

Jérôme Desrame

Oncology Department, Jean Mermoz Private Hospital, Lyon, France

F

François Ghiringhelli

N

Nicolas Paleiron

Pneumology Department, Saint-Anne Military Teaching Hospital, Toulon, France

A

Antoine Khalil

Department of Radiology, Neuroradiology Unit, Assistance Publique-Hôpitaux de Paris, Bichat-Claude Bernard University Hospital, Paris, France

L

Laurent Milot

Body and VIR Radiology Department, Hospices Civils de Lyon, Hospital Edouard Herriot, Lyon, France

O

Olivier Chevallier

Department of Radiology, Section of Musculoskeletal Imaging and Intervention, LE2I UMR CNRS 6306, François-Mitterrand University Hospital, Dijon, France

A

Anne Couvelard

Department of Pathology, Assistance Publique-Hôpitaux de Paris, Bichat-Claude Bernard University Hospital, Paris, France

S

Sylvie Lantuejoul

Department of Biopathology, Léon Bérard Centre, Lyon, France

A

Alexandra Langlais

Clinical Research Unit, Intergroupe Francophone de Cancérologie Thoracique, Paris, France

F

Franck Morin

M

Michaël Duruisseaux

Respiratory Department and Early Phase (EPSILYON), Louis Pradel Hospital, Hospices Civils de Lyon Cancer Institute, Lyon, France

P

Pierre Michel

Hepatogastroenterology Department, Rouen University Hospital, Rouen, France

C

Christophe Louvet

Department of Medical Oncology, Institut Mutualiste Montsouris, Paris, France

V

Virginie Westeel

Pneumology department, CHU Besançon - Hôpital J. MINJOZ, Besançon, France

N

Nicolas Girard

Institut Curie, Institut du Thorax Curie-Montsouris, Paris