Inflammatory Waldenström macroglobulinemia is associated with clonal hematopoiesis: a multicentric cohort

P Pierre-Edouard Debureaux (1Leukemia Institute Paris Saint-Louis, Paris, France) S Stéphanie Poulain S Stephanie Harel (1APHP, Université Paris Cité, INSERM UMR 1342, Immno-hematologie, Paris, France) M Marie Passet (2Institut de Recherche Saint-Louis, Université Paris Cité, Paris, France) M Marie Templé (11Université de Paris Cité, Institut Cochin, Centre National de la Recherche Scientifique Unité Mixte de Recherche 8104, INSERM U1016, Paris, France) C Chloé Friedrich (7Hematobiology Unit, Cochin Hospital, Paris, France) N Nathalie Forgeard (2Saint Louis Hospital, Immuno-Hematology, Paris, France) D Dikelele Elessa (4Institut Paoli-Calmettes, Department of Hematology, Marseille, France) W William Plas (6Hematology Laboratory, Saint-Louis Hospital, Paris, France) L Laureen Chat (1Leukemia Institute Paris Saint-Louis, Paris, France) G Gregory Lazarian L Lise Willems (20CHU Cochin, Hematology, Paris, France) B Bruno Royer (2APHP, Paris, France) A Alexis Talbot (1APHP, Université Paris Cité, INSERM UMR 1342, Immno-hematologie, Paris, France) T Tristan Vaugeois (2Saint Louis Hospital, Immuno-Hematology, Paris, France) F Floriane Theves (2Saint Louis Hospital, Immuno-Hematology, Paris, France) A Alexandre Terre (7Tenon Hospital, Internal medecine, Paris, France) A Anne Brignier (8Saint Louis Hospital, Apheresis, Paris, France) M Marion Malphettes (9Saint Louis Hospital, Immuno Pathology, Paris, France) D Daphne Krzisch (10Saint Louis Hospital, Hemato-Oncology, Paris, France) L Laurent Frenzel F Frederic Davi (12Pitie Hospital, Laboratory of Hematology, Paris, France) C Clotilde Bravetti (16Department of Hematology, Pitié-Salpêtrière Hospital, Paris, France) F Florence Nguyen-Khac (31APHP, Paris, France) J Jehan Dupuis (5Hôpital Henri Mondor, Lymphoid Unit, Créteil, France) W Wendy Cuccuini (30Groupe Francophone de Cytogénétique Hématologique, Paris, France) D Didier Bouscary (19Department of Hematology, Cochin Hospital, Assistance Publique–Hôpitaux de Paris, Paris, France) O Olivier Hermine D Damien Roos-Weil (5Drug Resistance in Hematological Malignancies Team, Centre de Recherche des Cordeliers, Université Paris Cité, INSERM UMRS 1138, Sorbonne Université, Paris, France) O Olivier Kosmider (11Centre National de la Recherche Scientifique UMR8104, INSERM U1016, Institut Cochin, Université de Paris Cité, Paris, France) E Emmanuelle Clappier (2Institut de Recherche Saint-Louis, Université Paris Cité, Paris, France) M Marion Espéli K Karl Balabanian B Bertrand Arnulf (Hôpital Universitaire St. Louis, Assistance Publique–Hôpitaux de Paris (AP-HP), Paris)

Abstract

Abstract Inflammatory form of Waldenström macroglobulinemia (iWM) predicts outcomes after immuno-chemotherapy and Bruton tyrosine kinase inhibitors, but its origin is unknown. Here, we unravel increased clonal hematopoiesis in patients with iWM (61% vs 23% in noninflammatory WM), suggesting a contribution of environmental cells to iWM.

Article Details

Journal Blood
Volume / Issue Vol. 145, Issue 4
Published January 23, 2025
Pages 450-454
ISSN 0006-4971
Publisher Elsevier BV

Journal Info

Blood

Elsevier BV

ISSN: 0006-4971 Health Sciences

Authors (34)

P

Pierre-Edouard Debureaux

1Leukemia Institute Paris Saint-Louis, Paris, France

S

Stéphanie Poulain

S

Stephanie Harel

1APHP, Université Paris Cité, INSERM UMR 1342, Immno-hematologie, Paris, France

M

Marie Passet

2Institut de Recherche Saint-Louis, Université Paris Cité, Paris, France

M

Marie Templé

11Université de Paris Cité, Institut Cochin, Centre National de la Recherche Scientifique Unité Mixte de Recherche 8104, INSERM U1016, Paris, France

C

Chloé Friedrich

7Hematobiology Unit, Cochin Hospital, Paris, France

N

Nathalie Forgeard

2Saint Louis Hospital, Immuno-Hematology, Paris, France

D

Dikelele Elessa

4Institut Paoli-Calmettes, Department of Hematology, Marseille, France

W

William Plas

6Hematology Laboratory, Saint-Louis Hospital, Paris, France

L

Laureen Chat

1Leukemia Institute Paris Saint-Louis, Paris, France

G

Gregory Lazarian

L

Lise Willems

20CHU Cochin, Hematology, Paris, France

B

Bruno Royer

2APHP, Paris, France

A

Alexis Talbot

1APHP, Université Paris Cité, INSERM UMR 1342, Immno-hematologie, Paris, France

T

Tristan Vaugeois

2Saint Louis Hospital, Immuno-Hematology, Paris, France

F

Floriane Theves

2Saint Louis Hospital, Immuno-Hematology, Paris, France

A

Alexandre Terre

7Tenon Hospital, Internal medecine, Paris, France

A

Anne Brignier

8Saint Louis Hospital, Apheresis, Paris, France

M

Marion Malphettes

9Saint Louis Hospital, Immuno Pathology, Paris, France

D

Daphne Krzisch

10Saint Louis Hospital, Hemato-Oncology, Paris, France

L

Laurent Frenzel

F

Frederic Davi

12Pitie Hospital, Laboratory of Hematology, Paris, France

C

Clotilde Bravetti

16Department of Hematology, Pitié-Salpêtrière Hospital, Paris, France

F

Florence Nguyen-Khac

31APHP, Paris, France

J

Jehan Dupuis

5Hôpital Henri Mondor, Lymphoid Unit, Créteil, France

W

Wendy Cuccuini

30Groupe Francophone de Cytogénétique Hématologique, Paris, France

D

Didier Bouscary

19Department of Hematology, Cochin Hospital, Assistance Publique–Hôpitaux de Paris, Paris, France

O

Olivier Hermine

D

Damien Roos-Weil

5Drug Resistance in Hematological Malignancies Team, Centre de Recherche des Cordeliers, Université Paris Cité, INSERM UMRS 1138, Sorbonne Université, Paris, France

O

Olivier Kosmider

11Centre National de la Recherche Scientifique UMR8104, INSERM U1016, Institut Cochin, Université de Paris Cité, Paris, France

E

Emmanuelle Clappier

2Institut de Recherche Saint-Louis, Université Paris Cité, Paris, France

M

Marion Espéli

K

Karl Balabanian

B

Bertrand Arnulf

Hôpital Universitaire St. Louis, Assistance Publique–Hôpitaux de Paris (AP-HP), Paris