Ibrutinib in early stage CLL: Genetic risk factors and treatment outcome in the GCLLSG CLL12 trial

A Armin Riecke (German Military Hospital Ulm, Germany) S Sandra Robrecht (Department I of Internal Medicine, Center of Integrated Oncology Aachen Bonn Cologne Düsseldorf, University Hospital of Cologne, Cologne, Germany) D Deyan Yordanov Yosifov (German Cancer Research Center (DKFZ) Heidelberg, Germany) C Christof Schneider (Division of CLL, Department of Internal Medicine III, Ulm University, Ulm, Germany) A Adam Giza (1Faculty of Medicine and University Hospital Cologne, Department I of Internal Medicine, Center for Integrated Oncology Aachen Bonn Cologne Duesseldorf, German CLL Study Group, University of Cologne, Cologne, Germany) L Lothar Müller (Studienzentrum UnterEms, Leer, Germany) U Ursula Vehling-Kaiser (Day Clinic Hematology Oncology Palliative Care) M Michael J. Eckart (Hämatologie und Onkologie, Nürnberg, Germany) W Werner Freier (Medicinum, Hildesheim, Alabama, Germany) B Björn Schöttker (32Hämatologisch-Onkologische Schwerpunktpraxis Würzburg, Würzburg, Germany) T Tobias Gaska (Bruederkrankenhaus Paderborn, Paderborn, Germany) M Marcel Reiser (PIOH, Cologne, Germany) A Anna-Maria Fink (University Hospital of Cologne, Cologne, Germany) K Kirsten Fischer (Department I of Internal Medicine, Center of Integrated Oncology Aachen Bonn Cologne Düsseldorf, University Hospital of Cologne, Cologne, Germany) B Barbara F. Eichhorst (University of Cologne, Cologne, Germany) M Michael J Hallek (University of Cologne, Cologne, Germany) P Petra Langerbeins (University Hospital, Cologne, Germany) S Stephan Stilgenbauer (Division of CLL, Department of Internal Medicine III, Ulm University, Ulm, Germany) E Eugen Tausch (Division of CLL, Department of Internal Medicine III, Ulm University, Ulm, Germany)

Abstract

Watch & wait is the standard of care in asymptomatic early-stage chronic lymphocytic leukemia (CLL). The CLL12 trial investigated ibrutinib versus placebo in early-stage patients with intermediate to very high risk of progression, showing improved event-free survival (EFS) but no overall survival (OS) benefit10. Building on these findings, our analysis examined whether a significant benefit could be identified within distinct genetic subgroups. After a median follow-up of 69.3 months, there were 166 EFS and 32 OS events in 515 trial patients. In the placebo arm, del(17p), del(11q), +12, U-IGHV, and mutations in NOTCH1, ATM, NRAS/KRAS/BRAF, and NFKBIE correlated with shorter EFS. With ibrutinib, only del(17p) and TP53 and NFKBIE mutations significantly compromised EFS. Ibrutinib offered substantial EFS benefit in subgroups with U-IGHV, del(11q), +12, NOTCH1, ATM, and NFKBIE mutations. No EFS improvement was seen for asymptomatic early-stage patients with del(17p) or TP53 mutations. Ibrutinib provided no OS benefits in any genetic subgroup. Multivariable analysis revealed ibrutinib treatment as an independent favorable factor for EFS, while U-IGHV, del(17p), POT1, RAS/RAF, and NFKBIE mutations were adverse prognostic factors. The results confirm watch-and-wait as standard of care for early-stage CLL patients, especially in high-risk CLL characterized by del(17p) and/or mutated TP53. EudraCT Number: 2013-003211-22

Article Details

Journal Blood
Volume / Issue Vol. 1, Issue 1
Published June 18, 2026
ISSN 0006-4971
Publisher Elsevier BV

Journal Info

Blood

Elsevier BV

ISSN: 0006-4971 Health Sciences

Authors (19)

A

Armin Riecke

German Military Hospital Ulm, Germany

S

Sandra Robrecht

Department I of Internal Medicine, Center of Integrated Oncology Aachen Bonn Cologne Düsseldorf, University Hospital of Cologne, Cologne, Germany

D

Deyan Yordanov Yosifov

German Cancer Research Center (DKFZ) Heidelberg, Germany

C

Christof Schneider

Division of CLL, Department of Internal Medicine III, Ulm University, Ulm, Germany

A

Adam Giza

1Faculty of Medicine and University Hospital Cologne, Department I of Internal Medicine, Center for Integrated Oncology Aachen Bonn Cologne Duesseldorf, German CLL Study Group, University of Cologne, Cologne, Germany

L

Lothar Müller

Studienzentrum UnterEms, Leer, Germany

U

Ursula Vehling-Kaiser

Day Clinic Hematology Oncology Palliative Care

M

Michael J. Eckart

Hämatologie und Onkologie, Nürnberg, Germany

W

Werner Freier

Medicinum, Hildesheim, Alabama, Germany

B

Björn Schöttker

32Hämatologisch-Onkologische Schwerpunktpraxis Würzburg, Würzburg, Germany

T

Tobias Gaska

Bruederkrankenhaus Paderborn, Paderborn, Germany

M

Marcel Reiser

PIOH, Cologne, Germany

A

Anna-Maria Fink

University Hospital of Cologne, Cologne, Germany

K

Kirsten Fischer

Department I of Internal Medicine, Center of Integrated Oncology Aachen Bonn Cologne Düsseldorf, University Hospital of Cologne, Cologne, Germany

B

Barbara F. Eichhorst

University of Cologne, Cologne, Germany

M

Michael J Hallek

University of Cologne, Cologne, Germany

P

Petra Langerbeins

University Hospital, Cologne, Germany

S

Stephan Stilgenbauer

Division of CLL, Department of Internal Medicine III, Ulm University, Ulm, Germany

E

Eugen Tausch

Division of CLL, Department of Internal Medicine III, Ulm University, Ulm, Germany