Expansions of circulating plasmablasts producing commensal-reactive IgA antibodies are predictors for chronic GVHD

K Katharina M. Habenicht (1Division of Genetics, Department Biology, Friedrich-Alexander-Universität Erlangen-Nürnberg, Erlangen, Germany) J Jana Wanzek (1Friedrich-Alexander-Universität Erlangen-Nürnberg, Division of Genetics, Department Biology, Erlangen, Germany) A Anna Bootz (1Friedrich-Alexander-Universität Erlangen-Nürnberg, Division of Genetics, Department Biology, Erlangen, Germany) S Simon Schäfer (1Friedrich-Alexander-Universität Erlangen-Nürnberg, Division of Genetics, Department Biology, Erlangen, Germany) L Lara Vollmer (1Division of Genetics, Department Biology, Friedrich-Alexander-Universität Erlangen-Nürnberg, Erlangen, Germany) A Andreas Hiergeist M Matthias Fante (2University Hospital Regensburg, Department of Internal Medicine III, Hematology & Internal Oncology, Regensburg, Germany) J Jakob Hasenbank (1Division of Genetics, Department Biology, Friedrich-Alexander-Universität Erlangen-Nürnberg, Erlangen, Germany) A Andrea Schneider I Ingrid Vasova (1Friedrich-Alexander-Universität (FAU) Erlangen-Nürnberg and Universitätsklinikum Erlangen, Department of Internal Medicine 5 – Hematology and Oncology, Erlangen, Germany) S Silvia Spoerl (1Friedrich-Alexander-Universität (FAU) Erlangen-Nürnberg and Universitätsklinikum Erlangen, Department of Internal Medicine 5 – Hematology and Oncology, Erlangen, Germany) A Anna Brandt (2Department of Internal Medicine 5–Hematology and Oncology, Friedrich-Alexander-Universität Erlangen-Nürnberg and Universitätsklinikum Erlangen, Erlangen, Germany) M Michael Rehli P Petra Hoffmann S Stefan Wirtz (7Friedrich-Alexander-Universität Erlangen-Nürnberg and Universitätsklinikum Erlangen, Department of Internal Medicine 1 - Gastroenterology, Pneumology and Endocrinology, Erlangen, Germany) J Jesika Kotorri (8Institute of Clinical Microbiology, Immunology, and Hygiene, Friedrich-Alexander-Universität Erlangen-Nürnberg and Universitätsklinikum Erlangen, Erlangen, Germany) R Roman G. Gerlach (8Institute of Clinical Microbiology, Immunology, and Hygiene, Friedrich-Alexander-Universität Erlangen-Nürnberg and Universitätsklinikum Erlangen, Erlangen, Germany) A André Gessner A Andreas Mackensen (Friedrich-Alexander-Universität Erlangen–Nürnberg, Erlangen, Germany) J Julia Winkler (2Friedrich-Alexander-Universität Erlangen-Nürnberg and Universitätsklinikum Erlangen, Department of Internal Medicine 5 - Hematology and Oncology, Erlangen, Germany) D Daniel Wolff T Thomas H. Winkler (Division of Genetics, Department Biology, Friedrich-Alexander-Universität Erlangen-Nürnberg (FAU), Erlangen, Germany.)

Abstract

Abstract Chronic graft-versus-host disease (cGVHD) is characterized by dysregulation of the adaptive immune system, including an aberrant B-cell homeostasis after allogeneic hematopoietic stem cell transplantation (allo-SCT). It is uncertain, however, whether this B-cell dysregulation is a result of manifest cGVHD or develops as a sign of aberrant B lymphopoiesis after allo-SCT before cGVHD becomes apparent. To gain insight into the development of B-cell dysregulation before the onset of cGVHD, we analyzed B-cell subpopulations by multiparameter flow cytometry on days 90, 180, and 356 after allo-SCT in a prospective study design. After completion of follow-up, patients were assigned retrospectively to 3 groups according to onset of GVHD: (1) no GVHD (n = 17); (2) acute GVHD (aGVHD) without subsequent cGVHD (n = 32); and (3) cGVHD (n = 59). Although CD21lowCD11c+ B cells were increased in all groups, the frequency of CD20–CD38hi plasmablasts was significantly elevated already 90 days after allo-SCT in patients who subsequently developed cGVHD, compared to patients without GVHD or with aGVHD only (median of CD19+ cells, 5.9% vs 2.2% vs 2.2%; P = .0016 and .0304, respectively). Detailed molecular analysis of expanded plasmablasts revealed a dominance of the immunoglobulin A isotype, with molecular evidence for recent generation in mucosal sites and markers for intestinal homing. A large fraction of the clonally expanded plasmablasts produced antibodies that bound to subgroups of commensals known to produce short-chain fatty acids. In summary, our data suggest that dysregulated intestinal antibody responses against commensals contribute to the pathophysiology of cGVHD.

Article Details

Journal Blood
Volume / Issue Vol. 145, Issue 26
Published June 26, 2025
Pages 3178-3188
ISSN 0006-4971
Publisher Elsevier BV

Journal Info

Blood

Elsevier BV

ISSN: 0006-4971 Health Sciences

Authors (22)

K

Katharina M. Habenicht

1Division of Genetics, Department Biology, Friedrich-Alexander-Universität Erlangen-Nürnberg, Erlangen, Germany

J

Jana Wanzek

1Friedrich-Alexander-Universität Erlangen-Nürnberg, Division of Genetics, Department Biology, Erlangen, Germany

A

Anna Bootz

1Friedrich-Alexander-Universität Erlangen-Nürnberg, Division of Genetics, Department Biology, Erlangen, Germany

S

Simon Schäfer

1Friedrich-Alexander-Universität Erlangen-Nürnberg, Division of Genetics, Department Biology, Erlangen, Germany

L

Lara Vollmer

1Division of Genetics, Department Biology, Friedrich-Alexander-Universität Erlangen-Nürnberg, Erlangen, Germany

A

Andreas Hiergeist

M

Matthias Fante

2University Hospital Regensburg, Department of Internal Medicine III, Hematology & Internal Oncology, Regensburg, Germany

J

Jakob Hasenbank

1Division of Genetics, Department Biology, Friedrich-Alexander-Universität Erlangen-Nürnberg, Erlangen, Germany

A

Andrea Schneider

I

Ingrid Vasova

1Friedrich-Alexander-Universität (FAU) Erlangen-Nürnberg and Universitätsklinikum Erlangen, Department of Internal Medicine 5 – Hematology and Oncology, Erlangen, Germany

S

Silvia Spoerl

1Friedrich-Alexander-Universität (FAU) Erlangen-Nürnberg and Universitätsklinikum Erlangen, Department of Internal Medicine 5 – Hematology and Oncology, Erlangen, Germany

A

Anna Brandt

2Department of Internal Medicine 5–Hematology and Oncology, Friedrich-Alexander-Universität Erlangen-Nürnberg and Universitätsklinikum Erlangen, Erlangen, Germany

M

Michael Rehli

P

Petra Hoffmann

S

Stefan Wirtz

7Friedrich-Alexander-Universität Erlangen-Nürnberg and Universitätsklinikum Erlangen, Department of Internal Medicine 1 - Gastroenterology, Pneumology and Endocrinology, Erlangen, Germany

J

Jesika Kotorri

8Institute of Clinical Microbiology, Immunology, and Hygiene, Friedrich-Alexander-Universität Erlangen-Nürnberg and Universitätsklinikum Erlangen, Erlangen, Germany

R

Roman G. Gerlach

8Institute of Clinical Microbiology, Immunology, and Hygiene, Friedrich-Alexander-Universität Erlangen-Nürnberg and Universitätsklinikum Erlangen, Erlangen, Germany

A

André Gessner

A

Andreas Mackensen

Friedrich-Alexander-Universität Erlangen–Nürnberg, Erlangen, Germany

J

Julia Winkler

2Friedrich-Alexander-Universität Erlangen-Nürnberg and Universitätsklinikum Erlangen, Department of Internal Medicine 5 - Hematology and Oncology, Erlangen, Germany

D

Daniel Wolff

T

Thomas H. Winkler

Division of Genetics, Department Biology, Friedrich-Alexander-Universität Erlangen-Nürnberg (FAU), Erlangen, Germany.