Ex vivo venetoclax sensitivity predicts clinical response in acute myeloid leukemia in the prospective VenEx trial

S Sari Kytölä (1Department of Hematology, Helsinki University Hospital Comprehensive Cancer Center, Helsinki, Finland) I Ida Vänttinen (2Institute for Molecular Medicine Finland, HiLIFE, University of Helsinki, Helsinki, Finland) T Tanja Ruokoranta (1Department of Hematology, Helsinki University Hospital Comprehensive Cancer Center, Helsinki, Finland) A Anu Partanen (3Department of Medicine, Kuopio University Hospital, Kuopio, Finland) A Annasofia Holopainen (3Department of Medicine, Kuopio University Hospital, Kuopio, Finland) J Joseph Saad (2Institute for Molecular Medicine Finland, HiLIFE, University of Helsinki, Helsinki, Finland) M Milla E. L. Kuusisto (4Department of Hematology, University of Oulu, Oulu, Finland) S Sirpa Koskela (5Department of Internal Medicine, Tampere University Hospital, Tampere, Finland) R Riikka Räty (1Department of Hematology, Helsinki University Hospital Comprehensive Cancer Center, Helsinki, Finland) M Maija Itälä-Remes (6Turku University Hospital, Turku, Finland) I Imre Västrik (2Institute for Molecular Medicine Finland, HiLIFE, University of Helsinki, Helsinki, Finland) M Minna Suvela (1Institute for Molecular Medicine Finland - FIMM, HiLIFE, University of Helsinki, Helsinki, Finland) A Alun Parsons (2Institute for Molecular Medicine Finland, HiLIFE, University of Helsinki, Helsinki, Finland) K Kimmo Porkka (43Helsinki University Hospital Comprehensive Cancer Center, Hematology Research Unit Helsinki, University of Helsinki, Helsinki, Finland) K Krister Wennerberg C Caroline A. Heckman T Tero Jalkanen (8EstiMates Ltd, Turku, Finland) T Teppo Huttunen (8EstiMates Ltd, Turku, Finland) P Pia Ettala (58Department of Clinical Hematology and Stem Cells Transplantation Unit, Turku University Hospital and University of Turku, Turku, Finland) J Johanna Rimpiläinen (4Tampere University Hospital, Deparment of Internal Medicine, Tampere, Finland) T Timo Siitonen (6Cancer Center, Oulu University Hospital, Oulu, Finland) M Marja Pyörälä (5Kuopio University Hospital, Kuopio, Finland) H Heikki Kuusanmäki M Mika Kontro

Abstract

Abstract The B-cell lymphoma 2 inhibitor venetoclax has shown promise for treating acute myeloid leukemia (AML). However, identifying patients likely to respond remains a challenge, especially for those with relapsed/refractory (R/R) disease. We evaluated the utility of ex vivo venetoclax sensitivity testing to predict treatment responses to venetoclax-azacitidine in a prospective, multicenter, phase 2 trial. The trial recruited 104 participants with previously untreated (n = 48), R/R (n = 39), or previously treated secondary AML (sAML) (n = 17). The primary end point was complete remission or complete remission with incomplete hematologic recovery (CR/CRi) rate in ex vivo sensitive trial participants during the first 3 therapy cycles. The key secondary end points included the correlations between ex vivo drug sensitivity, responses, and survival. Venetoclax sensitivity was successfully assessed in 102 of 104 participants, with results available within a median of 3 days from sampling. In previously untreated AML, ex vivo sensitivity corresponded to an 85% (34/40) CR/CRi rate, with a median overall survival (OS) of 28.7 months, compared with 5.5 months for ex vivo resistant patients (P = .002). For R/R/sAML, ex vivo sensitivity resulted in a 62% CR/CRi rate (21/34) and median OS of 9.7 vs 3.3 months for ex vivo resistant patients (P < .001). In univariate and multivariate analysis, ex vivo venetoclax sensitivity was the strongest predictor for a favorable treatment response and survival. This trial demonstrates the feasibility of integrating ex vivo drug testing into clinical practice to identify patients with AML, particularly in the R/R setting, who benefit from venetoclax. This trial was registered at www.clinicaltrials.gov as #NCT04267081.

Article Details

Journal Blood
Volume / Issue Vol. 145, Issue 4
Published January 23, 2025
Pages 409-421
ISSN 0006-4971
Publisher Elsevier BV

Journal Info

Blood

Elsevier BV

ISSN: 0006-4971 Health Sciences

Authors (24)

S

Sari Kytölä

1Department of Hematology, Helsinki University Hospital Comprehensive Cancer Center, Helsinki, Finland

I

Ida Vänttinen

2Institute for Molecular Medicine Finland, HiLIFE, University of Helsinki, Helsinki, Finland

T

Tanja Ruokoranta

1Department of Hematology, Helsinki University Hospital Comprehensive Cancer Center, Helsinki, Finland

A

Anu Partanen

3Department of Medicine, Kuopio University Hospital, Kuopio, Finland

A

Annasofia Holopainen

3Department of Medicine, Kuopio University Hospital, Kuopio, Finland

J

Joseph Saad

2Institute for Molecular Medicine Finland, HiLIFE, University of Helsinki, Helsinki, Finland

M

Milla E. L. Kuusisto

4Department of Hematology, University of Oulu, Oulu, Finland

S

Sirpa Koskela

5Department of Internal Medicine, Tampere University Hospital, Tampere, Finland

R

Riikka Räty

1Department of Hematology, Helsinki University Hospital Comprehensive Cancer Center, Helsinki, Finland

M

Maija Itälä-Remes

6Turku University Hospital, Turku, Finland

I

Imre Västrik

2Institute for Molecular Medicine Finland, HiLIFE, University of Helsinki, Helsinki, Finland

M

Minna Suvela

1Institute for Molecular Medicine Finland - FIMM, HiLIFE, University of Helsinki, Helsinki, Finland

A

Alun Parsons

2Institute for Molecular Medicine Finland, HiLIFE, University of Helsinki, Helsinki, Finland

K

Kimmo Porkka

43Helsinki University Hospital Comprehensive Cancer Center, Hematology Research Unit Helsinki, University of Helsinki, Helsinki, Finland

K

Krister Wennerberg

C

Caroline A. Heckman

T

Tero Jalkanen

8EstiMates Ltd, Turku, Finland

T

Teppo Huttunen

8EstiMates Ltd, Turku, Finland

P

Pia Ettala

58Department of Clinical Hematology and Stem Cells Transplantation Unit, Turku University Hospital and University of Turku, Turku, Finland

J

Johanna Rimpiläinen

4Tampere University Hospital, Deparment of Internal Medicine, Tampere, Finland

T

Timo Siitonen

6Cancer Center, Oulu University Hospital, Oulu, Finland

M

Marja Pyörälä

5Kuopio University Hospital, Kuopio, Finland

H

Heikki Kuusanmäki

M

Mika Kontro