Efficacy and Safety of Anselamimab in Immunoglobulin Light Chain Amyloidosis: Results From the Randomized CARES Trials

A Ashutosh D. Wechalekar (National Amyloidosis Centre, University College London, Royal Free Hospital, London, United Kingdom.) V Victor H. Jimenez-Zepeda S Suzanne Lentzsch (Columbia University Medical Center, New York, New York, United States) E Eugene Scott Swenson Z Zilehuma Khan J Julia Catini H Hrishikesh Kulkarni (UCLA) B Brian Meltzer S Stephen Lake S Stephen Bek Ngie Ting P Peter Norman Mollee H Hermine Agis (Medical University of Vienna, Vienna) I Irene Strassl (20Ordensklinikum Linz, Linz, Austria) N Nathalie Meuleman (7Jules Bordet Institute, Hematology Department, Brussels, Belgium) M Michel Delforge V Victor Jimenez Zepeda S Shuyang Zhang (Institute of Molecular Medicine, Shanghai Key Laboratory for Nucleic Acid Chemistry and Nanomedicine) X Xin Du (State Key Laboratory of Immune Response and Immunotherapy, Department of Rheumatology and Immunology, The First Affiliated Hospital of University of Science and Technology of China, Center for Advanced Interdisciplinary Science and Biomedicine of IHM, Division of Life Sciences and Medicine, University of Science and Technology of China) J Jianan Wang H Honglan Qian (1The First Affiliated Hospital of Wenzhou Medical University, Department of Hematology, Wenzhou, China) C Chunyan Sun (School of Mathematics and Physics, Anqing Normal University 1 , Anqing 246133,) F František Sedlák A Arnaud Jaccard K Karim Belhadj (7Department of Hematology, Créteil Hospital, Assistance Publique–Hôpitaux de Paris, Paris, France) B Bertrand Arnulf (Hôpital Universitaire St. Louis, Assistance Publique–Hôpitaux de Paris (AP-HP), Paris) L Lionel Karlin (Service Hématologie, Hôpital Universitaire Lyon Sud, Pierre-Bénite, France) M Margaret Macro (Service Hématologie, Institut Hématologie de Basse Normandie, Hôpital Universitaire de Caen, Caen, France) J Jean-Marc Schiano De Colella (4Département Hématologie, Institut Paoli Calmettes, Marseille, France) A Anne-Marie Stoppa F Frank Bridoux T Thomas Chalopin J Jean-Francois Viallard (4Bordeaux University Hospital, Bordeaux, France) A Antoine Huart (Department of Nephrology and Transplantation, Toulouse Amyloidosis Center, Toulouse, France) A Alexander Carpinteiro R Roland Fenk (4University Hospital Düsseldorf, Department of Hematology, Oncology and Clinical Immunology, Düsseldorf, Germany) T Timon Hansen (Onkologicum HOPA, Hamburg, Hamburg, Germany) V Vera Girke A Axel Nogai E Efstathios Kastritis A Argiris (Anargyros) Symeonidis M Moshe Gatt (Hadassah Medical Cener, Hebrew University of Jerusalem, Jerusalem, Israel) N Noa Lavi (Department of Hematology, Rambam Health Care Campus, Haifa 3109601, Israel) H Hila Magen (Chaim Sheba Medical Center, Ramat-Gan, Israel) G Giovanni Palladini (Department of Molecular Medicine, University of Pavia, Italy (M.N., G.D.S., G.P.).) O Ombretta Annibali (Policlinico Universitario Campus Bio-Medico, Dipartimento di Medicina e Chirurgia Università Campus Bio-Medico, Rome) F Fabrizio Pane (4Hematology – Department of Clinical Medicine and Surgery, University Hospital “Federico II”, Napoli, Italy) G Gabriele Buda (Department of Clinical and Experimental Medicine, Hematology, University of Pisa, Pisa, Italy) T Tadao Ishida (Japanese Red Cross Medical Center, Tokyo) K Kenshi Suzuki S Shinsuke Iida T Takayuki Ikezoe (3Fukushima Medical University School of Medicine, Hematology, Fukushima, Japan) K Krzysztof Jamroziak (Medical University of Warsaw, Warsaw, Poland) J Jamin Byun Y Youngil Koh (Seoul National University Hospital, Seoul National University, Jongno-gu, Seoul, South Korea) K Kihyun Kim (Division of Hematology–Oncology, Department of Medicine, Sungkyunkwan University School of Medicine, Samsung Medical Center, Seoul, South Korea) R Ramon Lecumberri Villamediana M Maria Teresa Cibeira López (1Hospital Clinic of Barcelona, Barcelona, Spain) I Irene Romera Martinez R Rafael F. Duarte R Rafael Ríos (7Hospital Universitario Puerta de Hierro, Majadahonda, Spain) I Isabel Angela Krsnik Castello M María Esther Gonzalez García (26Hematology Department, Hospital Universitario de Cabueñes, Gijon, Spain) E Eusebio Narciso Martin Chacon J Javier Alberto Rojas Martinez A Ashutosh Wechalekar (National Amyloidosis Centre, London, United Kingdom) J Jason Valent (Cleveland Clinic Foundation, Cleveland, Ohio, United States) M Michaela Liedtke M Michael A. Rosenzweig A Alfred Chung (6University of California San Francisco, San Francisco, United States) S Sandy Wong (10Bristol Myers Squibb, Princeton, United States) N Naresh Bumma (Division of Hematology, The Ohio State University Comprehensive Cancer Center, Columbus, Ohio, United States) D Divaya Bhutani (Columbia University Medical Center, New York) G Giada Bianchi R Raymond Comenzo (Tufts Medical Center, Boston, Massachusetts, United States) M Mahmoud Gaballa (4The University of Texas MD Anderson Cancer Center, Houston, United States) H Hans C. Lee (1Department of Lymphoma and Myeloma, The University of Texas MD Anderson Cancer Center, Houston, TX) G Gregory P. Kaufman E Eva Medvedova (Knight Cancer Institute, Oregon Health and Science University, Portland) F Frank Passero K Keith Stockerl-Goldstein (1Washington University School of Medicine, Division of Oncology, Department of Medicine, Saint Louis, United States) A Adam Waxman (University of Pennsylvania, Philadelphia, Pennsylvania, United States) V Vaishali Sanchorawala (Boston University Chobanian & Avedisian School of Medicine and Boston Medical Center, Boston, Massachusetts, United States) A Anita D'Souza (1Medical College of Wisconsin, Milwaukee, United States) A Andrew Cowan (3University of Washington and Fred Hutchinson Cancer Center, Seattle, United States) S Sarah Lee (Department of Neurology and Neurological Sciences, Stanford University School of Medicine, Stanford, CA) E Edward Libby (3University of California, San Diego, San Diego, United States) A Angela Dispenzieri A Amandeep Godara (University of Utah School of Medicine, Salt Lake City, Utah, United States) T Tibor Kovacsovics (9City of Hope, Goodyear, United States) S Salyka M. Sengsayadeth S Stacey Ann Goodman C Chakra Chaulagain (Department of Hematology and Oncology, Myeloma and Amyloidosis Program, Cleveland Clinic Florida, Weston)

Abstract

PURPOSE In immunoglobulin light chain (AL) amyloidosis, amyloid fibrils cause organ dysfunction. Anselamimab, a monoclonal antibody, selectively binds to amyloid fibrils, accelerating their clearance. METHODS Newly diagnosed patients with European modification of Mayo 2004 stage IIIa or IIIb AL amyloidosis were randomly assigned to receive anselamimab or placebo with cyclophosphamide, bortezomib, and dexamethasone (with or without daratumumab). The primary end point was a hierarchical composite of time to all-cause mortality (ACM) and frequency of cardiovascular hospitalizations (CVHs), analyzed using the Finkelstein-Schoenfeld test and win ratio estimation. RESULTS Among 406 randomly assigned patients, the primary end point win ratio for anselamimab versus placebo was 1.11 (95% CI, 0.83, 1.50; P = .332) and the hazard ratio (HR) for ACM was 0.80 (95% CI, 0.57, 1.13; P = .290). CVH rates in the anselamimab and placebo groups were 0.59 (95% CI, 0.42, 0.83) and 0.89 (95% CI, 0.55, 1.43), respectively ( P = .145). Among patients with kappa isotype (n = 72), the win ratio was 2.06 (95% CI, 0.98, 4.31; P = .100) and anselamimab reduced ACM by 62% versus placebo (HR, 0.38; 95% CI, 0.17 to 0.86; nominal P = .012), and CVH by 71% (IRR, 0.29; 95% CI, 0.10 to 0.87; nominal P = .028) with improvements in Kansas City Cardiomyopathy Questionnaire-Overall Score. There was no clinical benefit observed in the lambda population. Anselamimab was generally well-tolerated; safety data were comparable between treatment arms overall. CONCLUSION Treatment with anselamimab, an antifibril antibody used alongside antiplasma cell dyscrasia therapy, while not meeting the primary end point in the overall population, significantly improved ACM and CVH in patients with kappa AL, potentially offering a new therapeutic option for this isotype.

Article Details

Volume / Issue Vol. 44, Issue 20
Published July 10, 2026
Pages 1899-1910
ISSN 0732-183X
Publisher Lippincott Williams & Wilkins

Journal Info

Journal of Clinical Oncology

Lippincott Williams & Wilkins

ISSN: 0732-183X Health Sciences

Authors (92)

A

Ashutosh D. Wechalekar

National Amyloidosis Centre, University College London, Royal Free Hospital, London, United Kingdom.

V

Victor H. Jimenez-Zepeda

S

Suzanne Lentzsch

Columbia University Medical Center, New York, New York, United States

E

Eugene Scott Swenson

Z

Zilehuma Khan

J

Julia Catini

H

Hrishikesh Kulkarni

UCLA

B

Brian Meltzer

S

Stephen Lake

S

Stephen Bek Ngie Ting

P

Peter Norman Mollee

H

Hermine Agis

Medical University of Vienna, Vienna

I

Irene Strassl

20Ordensklinikum Linz, Linz, Austria

N

Nathalie Meuleman

7Jules Bordet Institute, Hematology Department, Brussels, Belgium

M

Michel Delforge

V

Victor Jimenez Zepeda

S

Shuyang Zhang

Institute of Molecular Medicine, Shanghai Key Laboratory for Nucleic Acid Chemistry and Nanomedicine

X

Xin Du

State Key Laboratory of Immune Response and Immunotherapy, Department of Rheumatology and Immunology, The First Affiliated Hospital of University of Science and Technology of China, Center for Advanced Interdisciplinary Science and Biomedicine of IHM, Division of Life Sciences and Medicine, University of Science and Technology of China

J

Jianan Wang

H

Honglan Qian

1The First Affiliated Hospital of Wenzhou Medical University, Department of Hematology, Wenzhou, China

C

Chunyan Sun

School of Mathematics and Physics, Anqing Normal University 1 , Anqing 246133,

F

František Sedlák

A

Arnaud Jaccard

K

Karim Belhadj

7Department of Hematology, Créteil Hospital, Assistance Publique–Hôpitaux de Paris, Paris, France

B

Bertrand Arnulf

Hôpital Universitaire St. Louis, Assistance Publique–Hôpitaux de Paris (AP-HP), Paris

L

Lionel Karlin

Service Hématologie, Hôpital Universitaire Lyon Sud, Pierre-Bénite, France

M

Margaret Macro

Service Hématologie, Institut Hématologie de Basse Normandie, Hôpital Universitaire de Caen, Caen, France

J

Jean-Marc Schiano De Colella

4Département Hématologie, Institut Paoli Calmettes, Marseille, France

A

Anne-Marie Stoppa

F

Frank Bridoux

T

Thomas Chalopin

J

Jean-Francois Viallard

4Bordeaux University Hospital, Bordeaux, France

A

Antoine Huart

Department of Nephrology and Transplantation, Toulouse Amyloidosis Center, Toulouse, France

A

Alexander Carpinteiro

R

Roland Fenk

4University Hospital Düsseldorf, Department of Hematology, Oncology and Clinical Immunology, Düsseldorf, Germany

T

Timon Hansen

Onkologicum HOPA, Hamburg, Hamburg, Germany

V

Vera Girke

A

Axel Nogai

E

Efstathios Kastritis

A

Argiris (Anargyros) Symeonidis

M

Moshe Gatt

Hadassah Medical Cener, Hebrew University of Jerusalem, Jerusalem, Israel

N

Noa Lavi

Department of Hematology, Rambam Health Care Campus, Haifa 3109601, Israel

H

Hila Magen

Chaim Sheba Medical Center, Ramat-Gan, Israel

G

Giovanni Palladini

Department of Molecular Medicine, University of Pavia, Italy (M.N., G.D.S., G.P.).

O

Ombretta Annibali

Policlinico Universitario Campus Bio-Medico, Dipartimento di Medicina e Chirurgia Università Campus Bio-Medico, Rome

F

Fabrizio Pane

4Hematology – Department of Clinical Medicine and Surgery, University Hospital “Federico II”, Napoli, Italy

G

Gabriele Buda

Department of Clinical and Experimental Medicine, Hematology, University of Pisa, Pisa, Italy

T

Tadao Ishida

Japanese Red Cross Medical Center, Tokyo

K

Kenshi Suzuki

S

Shinsuke Iida

T

Takayuki Ikezoe

3Fukushima Medical University School of Medicine, Hematology, Fukushima, Japan

K

Krzysztof Jamroziak

Medical University of Warsaw, Warsaw, Poland

J

Jamin Byun

Y

Youngil Koh

Seoul National University Hospital, Seoul National University, Jongno-gu, Seoul, South Korea

K

Kihyun Kim

Division of Hematology–Oncology, Department of Medicine, Sungkyunkwan University School of Medicine, Samsung Medical Center, Seoul, South Korea

R

Ramon Lecumberri Villamediana

M

Maria Teresa Cibeira López

1Hospital Clinic of Barcelona, Barcelona, Spain

I

Irene Romera Martinez

R

Rafael F. Duarte

R

Rafael Ríos

7Hospital Universitario Puerta de Hierro, Majadahonda, Spain

I

Isabel Angela Krsnik Castello

M

María Esther Gonzalez García

26Hematology Department, Hospital Universitario de Cabueñes, Gijon, Spain

E

Eusebio Narciso Martin Chacon

J

Javier Alberto Rojas Martinez

A

Ashutosh Wechalekar

National Amyloidosis Centre, London, United Kingdom

J

Jason Valent

Cleveland Clinic Foundation, Cleveland, Ohio, United States

M

Michaela Liedtke

M

Michael A. Rosenzweig

A

Alfred Chung

6University of California San Francisco, San Francisco, United States

S

Sandy Wong

10Bristol Myers Squibb, Princeton, United States

N

Naresh Bumma

Division of Hematology, The Ohio State University Comprehensive Cancer Center, Columbus, Ohio, United States

D

Divaya Bhutani

Columbia University Medical Center, New York

G

Giada Bianchi

R

Raymond Comenzo

Tufts Medical Center, Boston, Massachusetts, United States

M

Mahmoud Gaballa

4The University of Texas MD Anderson Cancer Center, Houston, United States

H

Hans C. Lee

1Department of Lymphoma and Myeloma, The University of Texas MD Anderson Cancer Center, Houston, TX

G

Gregory P. Kaufman

E

Eva Medvedova

Knight Cancer Institute, Oregon Health and Science University, Portland

F

Frank Passero

K

Keith Stockerl-Goldstein

1Washington University School of Medicine, Division of Oncology, Department of Medicine, Saint Louis, United States

A

Adam Waxman

University of Pennsylvania, Philadelphia, Pennsylvania, United States

V

Vaishali Sanchorawala

Boston University Chobanian & Avedisian School of Medicine and Boston Medical Center, Boston, Massachusetts, United States

A

Anita D'Souza

1Medical College of Wisconsin, Milwaukee, United States

A

Andrew Cowan

3University of Washington and Fred Hutchinson Cancer Center, Seattle, United States

S

Sarah Lee

Department of Neurology and Neurological Sciences, Stanford University School of Medicine, Stanford, CA

E

Edward Libby

3University of California, San Diego, San Diego, United States

A

Angela Dispenzieri

A

Amandeep Godara

University of Utah School of Medicine, Salt Lake City, Utah, United States

T

Tibor Kovacsovics

9City of Hope, Goodyear, United States

S

Salyka M. Sengsayadeth

S

Stacey Ann Goodman

C

Chakra Chaulagain

Department of Hematology and Oncology, Myeloma and Amyloidosis Program, Cleveland Clinic Florida, Weston