Constitutive inflammation and epithelial-mesenchymal transition dictate sensitivity to nivolumab in CONFIRM: a placebo-controlled, randomised phase III trial

D Dean A. Fennell K Kayleigh Hill M Min Zhang C Charlotte Poile S Sean Ewings E Essa Y. Baitei J Joanna Dzialo N Nada Nusrat J Jan Rogel D Daniel Faulkner C Christian Ottensmeier R Raffaele Califano G Gerard G. Hanna S Sarah Danson N Nicola Steele M Mavis Nye L Lucy Johnson K Kim Mallard J Joanne Lord C Calley Middleton P Peter Szlosarek S Sam Chan L Liz Darlison P Peter Wells-Jordan C Cathy Richards J James Harber A Aleksandra Bzura J Jake Spicer C Catrin Pritchard T Tamihiro Kamata J Jens C. Hahne M Maymun Jama E Edward J. Hollox J Jason F. Lester J Jin-Li Luo Z Zisen Zhou H Hongji Yang H Huiyu Zhou A Astero Klampatsa G Gareth O. Griffiths

Abstract

Abstract Leveraging adaptive tumour immunity to control mesothelioma via immune checkpoint blockade is now a standard therapeutic approach. However, the determinants of sensitivity remain elusive. Low non-synonymous mutation burden and programmed death-ligand 1 expression, an abundance of immunosuppressive immune cell infiltration, and 9p21 deletion should all mitigate responses to therapy. To address this knowledge gap, we conducted a double blind, placebo-controlled, randomized phase III trial of the PD1 inhibitor, nivolumab (ClinicalTrial.gov registration: NCT03063450). After 37.2 months of follow-up, the primary endpoint of progression free-survival, but not overall survival was met. The nivolumab response rate was 10.3%, and related grade 3 or above adverse events occurred in 20.4% versus 7.2% for placebo. Progression-free and overall survival were longer in nivolumab-treated responders versus non-responders. In an exploratory multiomic analysis, blinded whole exome, transcriptome and multiplex immune profiling were used to interrogate R- versus NR-subgroups. Non-synonymous and neoantigen mutation burden were no different between groups, however R-mesotheliomas were infiltrated with activated CD8+ T- and CD19+ B-lymphocytes, organised into tertiary lymphoid structures. B-cell infiltration correlated with pro-inflammatory chemokines including IL24 and CCL19. Conversely, epithelial-mesenchymal transition and mitosis were associated with resistance to nivolumab. These findings illuminate features which can be leveraged to advance precision immunotherapy in this rare cancer setting.

Article Details

Volume / Issue Vol. 16, Issue 1
Published July 21, 2025
ISSN 2041-1723
Publisher Nature Portfolio

Journal Info

Nature Communications

Nature Portfolio

ISSN: 2041-1723 Open Access Life Sciences

Authors (40)

D

Dean A. Fennell

K

Kayleigh Hill

M

Min Zhang

C

Charlotte Poile

S

Sean Ewings

E

Essa Y. Baitei

J

Joanna Dzialo

N

Nada Nusrat

J

Jan Rogel

D

Daniel Faulkner

C

Christian Ottensmeier

R

Raffaele Califano

G

Gerard G. Hanna

S

Sarah Danson

N

Nicola Steele

M

Mavis Nye

L

Lucy Johnson

K

Kim Mallard

J

Joanne Lord

C

Calley Middleton

P

Peter Szlosarek

S

Sam Chan

L

Liz Darlison

P

Peter Wells-Jordan

C

Cathy Richards

J

James Harber

A

Aleksandra Bzura

J

Jake Spicer

C

Catrin Pritchard

T

Tamihiro Kamata

J

Jens C. Hahne

M

Maymun Jama

E

Edward J. Hollox

J

Jason F. Lester

J

Jin-Li Luo

Z

Zisen Zhou

H

Hongji Yang

H

Huiyu Zhou

A

Astero Klampatsa

G

Gareth O. Griffiths